Head and Neck Lecture for

Junior Medical Students

Shawn D. Newlands, M.D., Ph.D.

 

Introduction – (Slides 1-2)

 

Evaluation of Neck Masses – (Slide 3)

u     Adult

    “Neck mass in an adult present longer than one week is cancer until proven otherwise.”

u     Pediatric

    Less likely malignant

 

 Probably the most important thing for you to take away from this lecture is that a neck mass in an adult that is present for longer than a week, is cancer until proven otherwise.  About 90% of all adult neck masses are malignant, whereas the pediatric population neck masses are much more rarely malignant.

 

 

Etiology of Neck Masses – (Slides 4-5)

u     Congenital

»   Branchial cleft cyst

»   Thyroglossal duct cyst

»   Cystic hygroma (lymphangioma)

u     Inflammatory

»   Viral, Bacterial, Mycobacteria (Scrofula)

u     Acquired

»   Ranula, Laryngocele

u     Neoplastic - Benign

»   Lipoma, Hemangioma, Carotid body tumor, Salivary gland

u     Malignant

    Metastatic

»   Aerodigestive squamous cell - >95%

»   Skin CA

»   Distant sites

»   Sinonasal

»   Parotid

»   Melanoma

    Primary

»   Lymphoma

»   Sarcoma

»   Thyroid / Parathyroid

»   Salivary

 

 

 Like most things in medicine, they can be categorized based on their origin as being congenital, inflammatory, acquired or neoplastic.  This list is by no means comprehensive, but is just a taste of some of the etiologies that you might run across.  Congenital neck masses, although they are primarily first noticed in the pediatric population, are often not diagnosed or do not become apparent until the patient is in adulthood. 

Patients with brachial cleft cysts may not present until they’re in their fourth or fifth decade of life, so these lesions are in the differential diagnosis in both pediatric and adult population.  Branchial cleft cysts originate from the failure of pharyngobranchial ducts to become obliterated during early development.  They usually present when they become swollen after the patient suffers from a cold or other upper respiratory infection.  They’re characteristically fluctuant in nature and have a cystic feel which helps to differentiate them from more solid lesions.  The most common source is the second branchial cleft.  These cysts tend to be just anterior to the sternocleidomastoid muscle.  Treatment is excision.  ((Slide 10)

Thyroglossal duct cysts arise from a remnant left as the thyroid gland that descends from the floor of the pharynx, which becomes the base of the tongue, between 4 ½ and 6 weeks of development.  This tract travels either superficial to, through or just deep to the hyoid and reaches the foramen caecum.  These cysts also often present after an upper respiratory infection and may not present until the patient is in young adulthood.  Treatment is excision with the tract.  The operation for thyroglossal duct cysts includes removal of the center portion of the hyoid bone to reduce the likelihood that the entire cyst is excised which reduces the likelihood of recurrence.  This operation is the Sistrunk procedure and is best performed after any acute infection has resolved.  (Slide 11)

A cystic hygroma is also known as a lymphangioma.  It’s an abnormality in development of regional lymphatics.  Ninety-percent of these tumors occur before the end of the second decade of life and they seldom regress.  They often enlarge after upper respiratory tract infection.  Treatment is surgical excision.  Like the neck dissections, this operation involves removing the lymphatic bearing tissue and leaving non-lymphatic structures, such as nerves and large blood vessels, intact.  (Slides 6-9)

Hemangioma is the single most common head and neck neoplasm in children.  Hemangiomas often regress and are best treated conservatively but sometimes need resection.  (Slide 12)

In children, most cervical lymphadenopathy is inflammatory in nature.  This is often in response to a viral infection.  The viruses such as HIV and Epstein Barr virus can also cause cervical adenopathy. 

Suppurative infections of the cervical lymph nodes following upper respiratory tract infection are very common in young children and often need to be drained.  Mycobacterial infection is suspected when suppurative lymph nodes in the neck do not resolve rapidly with antibiotics.  You can also acquire neck masses such as ranula, which is from an obstructed sublingual duct.  This can present in the neck as a cystic mass.

A laryngocele is caused by blockage of the ventricle and the larynx, which can balloon out of the laryngeal framework and into the neck.  This is seen in trumpet players and glass blowers and is rarely seen in children. 

The neoplastic neck masses include benign masses such as lipomas and carotid body tumors, which are also called chemodectomas.  In adults the most common source of neck masses is neoplasm.  These are generally metastatic from the aerodigestive tract.  We will talk about this at length later in this lecture.

Metastatic neoplasms to the neck are almost always in the lymph nodes.  Squamous cell or basal cell carcinoma from the face and scalp can metastasize to neck lymph nodes.  Occasionally you will see metastasis from a distant site to a cervical lymph node, particularly GI and lung primaries to supraclavicular nodes. 

Parotid tumors and melanomas of the head and neck also metastasize to neck lymph nodes. 

Primary tumors in the neck include lymphomas, sarcomas and thyroid cancer.

 

 

Neck Mass – History – (Slides 13-17)

u     Duration

    Years - congenital

    Months - neoplastic

    Weeks

    Days - inflammatory

u     Pain

    Neck

    Otalgia

    Odynophagia

u     Size

    Increasing steadily

    Fluctuates

u     Hoarseness

u     Weight loss

u     Hemoptysis

u     Dysphagia

u     Respiratory distress

u     Halitosis

u     Family History

    Cancer

    MEN syndrome

    Chinese (Cantonese)

u     Past Medical/Surgical History

    Head and Neck Radiation

    Trauma

    Previous cancer

»   “Field cancerization”

u     Social History

    HIV Risks

    Tobacco

»   Smoking

»   Chewing

    Ethanol

    Occupational Exposures

»   Woodworkers

»   Radium

»   Nickel

    EBV

    Sun exposure

 

One item on the history, which is extremely helpful in trying to develop a differential diagnosis for neck mass, is the duration during which the neck mass is present.  Something is present for less than 7 days, then it’s likely to be inflammatory; if it’s present from 7 days to 7 years, it’s likely neoplastic; and for 7 years or longer, it’s likely a congenital.  Obviously, there’s a lot of overlap in these categorizations, but again, especially in adults, if you have a neck mass which has been present for more than a week that really needs to be worked up aggressively.  Too often we see delays, the patient is treated with antibiotics, etc., and during that time, if they do have head and neck cancer, this could significantly affect their prognosis.  When you are interviewing a patient with a neck mass, obviously there are a number of questions you ask besides just about the duration of the mass.  One is whether it hurts.  Sometimes people will complain of pain that is actually where the mass is.  Other people will complain of ear pain; that’s a very important sign in head and neck oncology.  Because the vagus nerve has some cutaneous intervention in the ear as well as in the pharynx, cancer pain from the lateral pharyngeal wall and tonsillar region perceived as otalgia.  Pain on swallowing obviously is a sign for throat cancer as well.  Other things we ask about are how the size of the lesion has changed over time.  A neck mass that increases steadily over time in an adult is very likely to be cancer whereas a lymph node that fluctuates is more likely to be infectious or perhaps an inflamed branchial cleft cyst or something of that sort. 

Hoarseness is an indication of a laryngeal or supraglottic lesion.  Most patients with head and neck cancer suffer from weight loss.  This is often a result of mechanical difficulty in eating, pain on eating and cachexia from having a tumor.  Sometimes these lesions will bleed, and the patient will complain of hemoptysis.  Difficulty swallowing due to obstruction is often present, especially in cervical esophageal tumors.   Respiratory stress, both by patient report and just by listening to the patient for stridor, will give you an indication if the patient might have a laryngeal lesion.  And lastly, a number of these cancer patients, you’ll notice if you’re in the cancer clinic for any time at all, have a characteristic “tumor smell,” which is basically the smell of necrotic tumor in their mouth, which is a tip-off also to a head and neck cancer.  Do not be fooled by the patient’s history.  They often “just noticed” a mass which we know has been there longer than they claim it has.  Likewise, a history of hoarseness from yelling may be do to cancer and the yelling just brought it to the patient’s attention.

Like with all aspects of medicine that you learn about, past medical and surgical histories are important.  You should ask about a family history for cancer.  A patient with a medullary carcinoma may have a M.E.N. or multiple endocrine neoplasm syndrome.  People who have recently emigrated from China, particularly the region of Canton, would be at much higher risk for nasopharyngeal carcinoma.  Nasopharyngeal carcinoma accounts for about 18% of cancer in these areas, whereas in the United States it’s well less than .5%.  There are people who, in the 1950s and ‘60s received radiation therapy for acne treatment.  These people have increased risk for papillary carcinoma of the thyroid.

One of the first things we always ask about is tobacco and ethanol use.  The incidents of head and neck cancer in people who smoke is in the neighborhood of 20 to 30 times greater than in nonsmokers, and the combined use of smoking and ethanol increases your risk a hundred-fold for these lesions. Certainly people who have had head and neck cancer in the past which has been treated, are at increased risk for either a recurrence of that same cancer or development of another cancer.  This is attributed to a concept coined field cancerization.  Basically, patients with mucosal carcinomas from smoking and ethanol use have damage to the surrounding mucosa.  This mutagenic damage predisposes them to second and even third or fourth primary tumors.  

Occupational exposures can also be very important.  Woodworkers, especially with softwood, who do not use filtration masks, have a very high incidence of adenocarcinoma of the sinuses.  In the past, those glow-in-the-dark watch dials were painted with radium and the people who painted those watch dials and watch hands would lick the paint brush on their tongue and they had a high incidence of tongue carcinoma.  Nickel is also correlated with carcinoma of the sinuses, and Epstein Barr virus is correlated with one type of nasopharyngeal carcinoma. At least twice a year, I make a new diagnosis of HIV in a patient who previously did not know that they had this disease.  These patients present with either a bilateral swelling of the parotid glands or bilateral cervical adenopathy.

 

Head and Neck - Physical Exam – (Slides 18-19)

u     Thorough exam on all patients

u     External

    General

    Face

    Eyes

    Skin

    Neurological

»   Cranial nerves

»   Mental status

 

u     Internal

    Ears           Otoscope

    Nose         Nasal speculum*, endoscopes

    Oral Cavity   Tongue blades*, bimanual exam

    Nasopharynx    Small Mirror*, endoscopes, F.O.L.   

    Oral Pharynx    Tongue blades*

    Hypopharynx   Laryngeal mirror*, F.O.L.

    Larynx       Laryngeal mirror*, F.O.L.

 

u     * Requires Head Mirror

 

 

The physical exam starts with the head and neck exam.  It’s important that you perform a thorough exam on every patient.  This is particularly true in patients that have neck masses.  We start the head and neck exam with an external view of the head and neck.  General appearance, of course, is important.  Does the face have any lesions or does the patient have facial paralysis? Are the eyes present and moving normally and not bulging?  Look at the skin and often times it’s obvious what the patient is in there for.  Neurological status is important in head and neck exam.  Cranial nerve dysfunction is often a sign of some pathology along the course of the nerve and is often tip-off to lesions at the patient’s base of skull. 

We then exam the head and neck area internally with a number of different tools that are outlined on the slide.   Go in an order, such as the ears first, then the nose and then the throat, and in the throat we look in the oral cavity, the oropharynx, nasopharynx, the hypopharynx and larynx.  For all aspects of this exam, other than looking in the ears, a head mirror is required.  We use a nasal speculum to look inside the nasal cavity.  Oftentimes, if there is a high index of suspicion or we want to get a better look, we can use a rigid fiberoptic endoscope, which will give us an excellent view of the entire nasal cavity.  We can also look at the nasopharynx this way; alternatively, you can look at the nasopharynx by looking through the mouth and using a mirror to look upwards behind the soft palate into the nasopharynx.  We exam the oral cavity by moving things around using tongue blades.

The bi-manual exam is an often forgotten part of this exam, where your finger is inside the mouth to palpate the floor of the mouth with the other hand in the submandibular area.  This will help you feel lymph nodes in the floor of the mouth as well as abnormalities in the submandibular gland.  A laryngeal mirror is used to look at the hypopharynx and larynx.  Again, this requires a head mirror and some practice to master.  Alternatively, we can use a fiberoptic laryngoscope, which is abbreviated as F.O.L. on the slide.  This tool gives us an excellent view of the patient’s pharynx and larynx. 

 

Neck Examination – (Slide 20)

    Palpation

    Auscultation

    Observation

    Parotid Glands

-  Thyroid Gland

 

Levels in the Neck – (Slide 21-23)

u     I - Submandibular triangle

u     II - Upper jugular

»   Skull base to hyoid bone

u     III - Middle jugular

»   Hyoid bone to cricoid ring or omohyoid muscle

u     IV - Lower jugular

»   Cricoid ring or omohyoid muscle to the clavicle

u     V - Spinal accessory nerve lymphatic chain

»   Posterior triangle

u     VI - Paratracheal

 

 

The neck can also be examined using the various senses, including palpation, auscultation and observation.  Examination of the neck includes examination of the parotid glands and examination of the thyroid gland.  One very important concept in working up the neck mass, and head and neck oncology in general, is the concept of different levels in the neck.  Different levels of the neck contain different lymph nodes groups, and these lymph node groups drain different parts of the head and neck.  Therefore, the location of an enlarged lymph node in the head and neck will give you a clue as to where the pathology might be that is causing this.  Alternatively, if you discover a patient has head and neck cancer, these are the lymph nodes that you would pay the most attention to in trying to discern if they might have some metastatic disease.  Level one is the submandibular triangle, to correlate it with the triangles that you learned in gross anatomy.  The predominant lymphatic drainage from the head and neck occurs along the jugular vein.  The lymphatics along the jugular vein are divided into the upper, middle and lower jugular groups.  These correspond to Levels Two, Three and Four.  Depending on whether you’re at surgery or doing a physical exam externally, the borders of the different levels are slightly changed.  The juncture between the upper jugular and the middle jugular group (Levels II and III) is the hyoid bone and the cutoff between the middle jugular and the lower jugular groups (Levels III and IV) is either the cricoid ring, if you palpate externally, or the omohyoid muscle if you have the neck open.  The posterior triangle from the posterior border of the sternocleidomastoid muscle to the trapezius muscle down to the clavicle contains the spinal accessory lymphatic chain; this is Level Five.  Level Six includes the peritracheal lymph nodes. 

 

Other Lymph Node Groups – (Slide 24)

u     Submental

u     Preauricular

u     Postauricular

u     Suboccipital

u     Peri-parotid

u     Intra-parotid

u     Parapharyngeal

u     Retropharyngeal

 

 

There are other lymph node groups in the head and neck which are not in the levels discussed.  These are listed on this slide.  Actually, the submental lymph nodes, which are in the submental triangle, are considered part of the Level One lymph node group.  Preauricular and postauricular lymph nodes and suboccipital lymph nodes drain the scalp.  Lymph nodes both around and in the parotid gland, as well as lymph nodes surrounding the pharynx can all be involved in head and neck cancer, and need to be addressed or considered during treatment for head and neck cancer. 

 

Head and Neck - Lymph Drainage Patterns – (Slide 25)

u      Lower Lip            Submental

u      Scalp                    Parotid, Suboccipital

u      Parotid                 Levels I, II

u      Oral cavity           Levels I, II, III

u      Oral Pharynx        Levels II, III, retro & parapharyngeal

u      Nasopharynx        Levels II, III, V

u      Hypopharynx      Levels II, III, IV, retro & parapharyngeal

u      Supraglottis           Levels II, III

u      Glottis                  Levels III, IV, VI

u      Thyroid                Levels III, IV, V, VI

u      Esophagus            Levels III, IV, V, VI

 

 

This list of drainage patterns seen in the head and neck is not comprehensive or exclusionary, and certain structures that are in the midline, including the nasopharynx, the soft palate and supraglottic larynx, tend to have bilateral lymph node drainage. Starting with the lower lip, that often drains to the submental triangle.  Lower lip cancers are often caused by pipe smoking or sun exposure.  Scalp lesions typically drain to the parotid and suboccipital nodes.  These are also commonly caused by sun exposure.  Primary tumors of the parotid gland drain to periparotid nodes as well as nodes in Levels One and Two.  Oral cavity tumors includes tumors of the tongue, floor of mouth, the gingiva, the retromolar trigone and the buccal mucosa tend to drain to Levels One, Two and Three.  The oral pharynx includes the soft palate, tonsil and the pharyngeal walls.  These areas drain to Levels Two and Three as well as to retro- and peri-pharyngeal lymph nodes.  The nasopharynx drains bilaterally, and it drains to Levels Two, Three and Five.  The hypopharynx, which is the pharynx below the level of the epiglottis and includes the pyriform sinuses, drains to Levels Two, Three and Four and also can drain to peripharyngeal and retropharyngeal lymph nodes.  The supraglottic larynx, which includes the epiglottis, aryepiglottic folds and arytenoids, drains to Levels Two and Three.  True glottic tumors, which are those of the true vocal cords, drain to Levels Three, Four and Six.  Thyroid tumors drain to Levels Three, Four, Five and Six.  And lastly, cervical esophageal cancers also drain to Levels Three, Four, Five and Six.  The most important thing to come away from this with is the concept of the specificity of the lymph node drainage to different areas of the aerodigestive tract. 

 

Neck Mass - Diagnostic Work-up – (Slides 26-27)

u     Biopsy lesions seen on physical exam

u     Fine needle aspiration of the lymph node

»   Very good sensitivity and good specificity for SCCA

»   No risk of cancer spread

»   Immediate feedback

u     Imaging

»   CT scan of the neck is “good standard”

»   MRI better for certain applications

u     Excision

»   Suspected lymphoma

»   Benign mass

»   Last resort for malignancy - prepared for neck dissection

u     CXR

»   Mets and second primaries

u     Labs

»   Nutrition, Metastasis

u     Other tests sometimes indicated

»   Chest CT

»   Barium swallow

»   Upper GI

»   Bone scan

»   Abdominal CT

»   Panoramic radiograph of the mandible

 

 Now, let’s suppose we have a patient who has presented to us with a neck mass.  This is an adult.  We’re suspicious of cancer, as we should be.  It’s slowly growing.  He complains of dysphagia and otalgia.  What are the things we need to do at this point?  Obviously, what we strive to do is to make a diagnosis and to help develop a treatment plan, and a number of things can be done at the initial visit.  One of the things we emphasize here, and most people who do head and neck cancer emphasize, is going ahead and trying to move expeditiously through the work-up.  The reason for this is, obviously, that the cancer is growing and has an increased chance to spread.  It’s difficult to get the patients into treatment very quickly with head and neck cancer, and that’s because there’s a number of tests that need to be ordered.  So, for these reasons, we like to a lot of this stuff done as soon as possible, so that we can move expeditiously through the work-up and get the person treated.  The easiest way to make diagnosis is to biopsy any lesions that are seen on physical exam.  So, if this patient with the lymph node has a necrotic ulcerative suspicious lesion on their tongue, you would go ahead and biopsy the tongue lesion and that would give you the diagnosis.  If you have a diagnosis of squamous cell carcinoma from the biopsy of the primary site, then there is no need to biopsy the lymph node. 

Now if, on your physical exam, you’re unable to find an obvious primary tumor, then of course you’ll want to know whether this really is a squamous cell carcinoma or is it some other lesion, either benign or malignant that requires a different work-up.  The best way to do this is to do a fine needle aspiration of the lymph node.  Fine needle aspiration, as it implies, involves placing a fine needle into the mass to get a number of cells for cytohistologic analysis.  Using a fine needle, there is virtually no risk of a cancer spread along the biopsy tract.  With cooperation from the pathologist, you can get a pretty good idea what the patient has immediately, which expedites treatment planning.  Any patient that we see in the clinic with a new head and neck cancer, with some exceptions, will get imaging; generally speaking a CT scan is the gold standard.  CT scan of the neck covers from the maxillary sinuses down to the thoracic inlet, and this is the standard CT scan that we order.  Occasionally we want to get a better view of the sinuses or the regions of the orbits, in which case, we would order a sinus CT.  CT scans are the gold standard for this purpose because, with contrast, it’s very easy to tell enlarged lymph nodes from blood vessels and it’s very good for detecting bone invasion.  Bone invasion is a particular concern with tumors of the oral cavity, which may involve the mandible or maxilla.  For certain applications including tongue tumors, the MRI may have some advantages, but generally speaking, the CT is the gold standard. 

Unless you have reason to suspect a lymphoma, based on fine needle aspiration and an ability to see a primary lesion, open excisional biopsy of neck nodes is generally frowned upon.  We would excise benign masses such as branchial cleft cysts or lipomas.  But in a squamous cell carcinoma or suspected malignancy of that sort, where the fine needle aspiration doesn’t provide enough data for a diagnosis, then open biopsy may be a diagnostic procedure of last resort.  You would send the lymph node for pathology from the operating room, and if the pathology is consistent with squamous cell carcinoma, you need to be prepared to complete a neck dissection.  The danger with an excisional biopsy of a lymph node with metastatic carcinoma in it is that you will spread the tumor through the incisions, and this is the reason why it’s recommended that you do a complete neck dissection at that time. 

At the time of the first visit, we will order a chest x-ray; we’re looking for metastatic disease from any squamous cell carcinoma as well as a primary lung tumor.  Although this section says neck mass diagnostic work-up, this diagnostic work-up is universal, really, for patients with suspected aerodigestive carcinoma, even if they do not have palpable lymphadenopathy.  We obtain blood labs, both for anticipated surgery as well as to assess the patient’s nutrition.  Most people will require liver function tests to look for evidence of metastasis.  Calcium levels and thyroid levels are checked if we are concerned about tumors from the thyroid/parathyroid gland.  Occasionally other tests are indicated.  A chest CT would be ordered if there was an abnormal chest x-ray or if there was a lot of lymphadenopathy low in the neck and you really wanted to look carefully to see if this has spread to the mediastinum.  A barium swallow is a good way to evaluate the esophagus, although oftentimes we’ll evaluate that by directly visualizing it, as we’ll talk about a couple of slides further on, when we talk about endoscopy.  It’s not infrequent that we evaluate someone with a supraclavicular node and the suspicion really is that they would have a carcinoma from below the clavicles, and upper GI or an abdominal CT may show the source of this tumor.  Renal cell carcinomas are also notorious for metastasizing to the head and neck.  We rarely get a bone scan; these sorts of tests for advanced metastases would be used only on patients with very advanced disease.  Panoramic x-rays of the mandible are often used to evaluate for bony erosion in patients with oral cavity cancer.

 

Work up of TxN+ - (Slides 28-29)

u     Imaging

u     Panendoscopy

»   Larynx

»   Pharynx

»   Esophagus

»   Bronchial tree

u     Directed biopsies

»   Tonsil

»   Nasopharynx

»   Base of Tongue

u     If truly Tx - Radiotherapy plus neck treatment

 

 

            A unique situation arises when you have a patient that has a lymph node in the neck, you’ve done a needle aspiration and you find it’s squamous cell carcinoma.  But you just can’t find the primary on physical exam.  Now, this happens about 5 – 10% of the time, and it’s what we call an unknown primary or TxN positive patient, somebody who has a tumor which is unknown and has a positive neck disease.  These people are evaluated with imaging after a thorough exam.  As we discussed a minute ago, a CT scan is usually used.  The next that’s done is a panendoscopy, or triple endoscopy.  This procedure involves a laryngoscopy, esophagoscopy and bronchoscopy to exam the larynx, the pharynx (including the nasopharynx), the esophagus and the bronchial tree.  Oftentimes, despite careful examination, you do not see the source of the cancer.  If you do see anything suspicious, that’s immediately biopsied, and if you can’t see anything on direct examination then removal of the tonsils, biopsy of the nasopharynx on both sides and the base of the tongue on both sides are indicated.  These structures are part of Waldeyer’s Ring, or the lymphatics of the aerodigestive tract, and they’re notorious for hiding small tumors in the crypts.  These tumors can metastasize while they’re still quite small at the primary location, but grow to be quite large in the regional lymphatics.  Now if the patient is truly Tx, meaning that even after this procedure you don’t find the source of the cancer, then you need to proceed with radiotherapy from nasopharynx to the clavicles to cover the whole aerodigestive tract.  The goal is to eliminate any small tumor that you couldn’t find.  In addition, you need to treat the neck disease; this will often involve a neck dissection, although often the neck can also be treated with radiotherapy.

 

Head and Neck Oncology – Treatment – (Slide 30)

u     Panendoscopy

    Staging

    Second primary (10%)

u     Surgery

u     Radiation Therapy

u     Chemotherapy

u     Multimodality therapy

u     Primary treatment vs. Neck treatment

u     Cure vs. Locoregional control

 

What is the treatment for head and neck cancer?  Well, first thing that we generally do is a panendoscopy.  (Slide 29) This is a procedure whereby we look at the entire aerodigestive tract.  We do this for two reasons.  The first is for staging.  Oftentimes, you can get a much better look at a lesion with the patient under anesthesia.  This is particularly true if it’s a hypopharyngeal, laryngeal or supraglottic lesion.  The second reason is that you’re looking for a second primary tumor.  Synchronous primary tumors, which are present at the diagnosis of the first cancer, are present 10% of the time in these patients.  This is a consequence of their risk factors and the concept of field cancerization I mentioned earlier.  They basically have failed the biological test for propensity to cancer in the sense that they’ve developed one cancer and therefore, they’re prone to develop others.  Oftentimes these second primary tumors are the lung, and that’s why a chest x-ray is so important.  On occasion, however, you find an unsuspected esophageal second primary, although we don’t find those all that often.  Sometime the panendoscopy is combined with the main surgery if it’s clear that surgery is the best initial treatment for the disease.

Head and neck oncology is an area that encompasses multiple medical specialties.  These include head and neck surgery, radiation therapy and medical oncology.  Especially for advanced tumors, multi-modality therapy is generally used.  Multi-modality therapy means that for one tumor you use two or more of the modalities mentioned: surgery, radiation therapy and/or chemotherapy.  At UTMB and a lot of other institutions, there is a head and neck tumor board.  This includes surgeons, radiation therapists, medical oncologists, head and neck radiologists and pathologists.  We meet and discuss all the head and neck cancer cases, and the group comes to a decision as to what the best treatment is.  This helps ensure the patient that they are getting the benefit of everybody’s expertise.  We don’t always use the same modality for both the primary and the neck disease.  For instance, the patient may have a very small tumor of the base of their tongue and significant disease in the neck.  This patient might undergo radiation only to their tongue base, but have radiation and a neck dissection to treat the neck disease. 

For many early lesions, surgery alone is an effective treatment modality.  For other early lesions, radiation alone is often used.  Chemotherapy alone is not an effective treatment modality and is only used as part of multimodality treatment for advanced lesions.

Another important consideration in head and neck oncologic treatment is difference between a cure and locoregional control.  Locoregional control is elimination of the tumor at the primary site and in the neck lymphatics.  While it’s always our goal to cure people who have head and neck cancer, this is a very deadly disease, and patients often present in advanced stages.  Generally speaking, therapy is better at controlling local and neck disease and a large number of these patients will eventually develop distant metastasis.  Thus, despite control of the cancer in their head and neck, they will not be cured.  This does not mean that these patients are not benefited by their treatment.  Death due to uncontrolled head and neck cancer is very unpleasant; it can be very disfiguring and require the patient to have a tracheotomy and a feeding tube.  Even if the patients eventually succumb to the disease, local regional control is a benefit in the patient’s quality of life. 

 

STAGE GROUPING (TNM) (Slide 31)

STAGE 0

Tis

N0

M0

STAGE I

T1

N0

M0

STAGE II

T2

N0

M0

STAGE III

T3

N0

M0

 

T1

N1

M0

 

T2

N1

M0

 

T3

N1

M0

STAGE IV-A

T4

N0

M0

 

T4

N1

M0

 

Any T

N2

M0

STAGE IV-B

Any T

N3

M0

STAGE IV-C

Any T

Any N

M1

 

Staging of head and neck cancer.  All cancer treatment really is subject to staging systems, and head and neck cancer is no exception.  The staging system varies from site to site, so the T staging for oral cavity is different from that in the oral pharynx and the hypopharynx.

The neck lymph node staging system is universal with the exception of nasopharyngeal cancers, and therefore is easier to remember.  What I’d like you to remember is the diagram above.  Based on the local T stage and the N stage, the overall staging correlates with survival.  Survival rates in head and neck cancer are measured at five years.  Properly treated, patients with Stage I disease have about a 90% 5-year survival rate.  Stage II disease generally corresponds with a 75% survival rate.  Stage III is 50%, and Stage IV is 25%.  As you can see, anybody has N2 neck disease, meaning either two or more lymph nodes, or a lymph node, more than 3 cm in size, is automatically a Stage IV.  So, the majority of patients who are presenting with a neck lymph node as a primary presenting symptom are either at least a Stage III, and usually Stage IV, disease.

 

Head & Neck Oncology - Surgical Treatment – (Slide 32)

u     Staging endoscopy

u     Neck dissection

u     Primary resection

u     Reconstruction

u     Airway management

u     Alimentary management

u     Wound care

 

 

The surgical treatment of head and neck cancer has a number of different aspects.  The first is the stage endoscopy that we talked about earlier.  The second is treatment of the primary disease.  This may require any of a very broad range of procedures; I’ll talk about some of them later in the lecture.  Suffice it to say that these operations are tailored to the location and size of the tumor.

An area that requires a lot of thought is handling of the cervical lymphatics.  Not every tumor requires neck dissection, but certainly the possibility of lymphatic spread to the neck, either or not adenopathy is present needs to be considered.

Now, anytime we do head and neck oncologic surgery, we’re concerned also about reconstructing the area to try to preserve function as much as possible, and generally speaking, function means speech and swallowing. 

We always go through a process of considering the airway management whenever we do head and neck cancer treatment.  This often involves tracheotomy, but not always, and sometimes this can be among the more difficult parts of the treatment regimen.  We also have to consider management of the patient’s nutrition.  Many of these patients are malnourished preoperatively because of the disease or possibly because of alcoholism.  And certainly the stress of surgery, as well as the inability to swallow because of surgery, needs to be taken into consideration.  The majority of these patients have working GI tracts, and so some way to bypass the upper digestive system is utilized generally to aliment the patient peri- and postoperatively.  And lastly, wound care is an issue in all surgery, and certainly head and neck surgery, where most of the time we operate in a surgical field full of spit, is no exception to this rule.

 

Neck Dissections – (Slides 33-36)

u     Purpose

    Staging

    Therapeutic

u     Type

    Extended Radical

    Radical

    Modified radical (save XI, Internal Jugular, and/or SCM)

    Functional

-   Selective

 

There are two different conceptual types of neck dissections that we do.  These are staging neck dissections, where basically there are no enlarged lymph nodes, but we’re taking out lymph nodes to see if there’s any microscopic disease.  If a patient has no neck disease, they’re staging is lower and therefore the prognosis is much better.  The second type of neck dissection is the therapeutic neck dissection.  This is one where you’re actually treating lymphatic spread with the neck dissection.

There are a number of different types of neck dissections that you’ll hear about, and I’ve listed the general types here, from the most radical to the most conservative.  In the early part of this century, Crile described the radical neck dissection.  This neck dissection was used for many years, regardless of the extent or location of lymph node disease being treated.  This original operation, which is a very good one, has been refined since that time.  A radical neck dissection is neck dissection whereby the contents of the neck Levels I – V are removed.  (Slide 34) The internal jugular vein, spinal accessory nerve, and sternocleidomastoid muscle are removed.  The vagus nerve, carotid artery, hypoglossal nerve, digastric muscle, and sympathetic truck are preserved.  (Slide 34) Now, if, in addition, if any of these five “preserved” structures are removed, that would make this an extended radical neck dissection.  A neck dissection is a modified neck dissection if you save the 11th cranial nerve, the internal jugular vein and/or the sternoclidomastoid muscle.  In a traditional modified radical, only the 11th nerve is saved, but there’s numbers for the different types of modified radical neck dissections.  (Slide 35)

Functional neck dissection is basically another way of categorizing modified radical neck dissections.  And lastly, we come to selective neck dissections.  Selective neck dissections mean that the lymph nodes from levels one through five are not removed, but that you have removed, say, just levels one, two and three, or two, three and four.  Selective neck dissections are used when you are operating on a neck that has no lymphadenopathy, and you’re doing it for staging purposes.  (Slide 36)

 

Primary Resection – (Slide 37)

u     Margins – Clear margins correlate with improved survival